This website hosted by the Netherlands Heart Institute is for information and training purpose only, The Netherlands Heart Institute nor the individual researchers involved in this project carry responsibility for medical decisions made with the information provided by this website.

The ARVC risk calculator is based on clinical data of patients fulfilling ARVC diagnosis as per modified Task Force Criteria (TFC) [1] from 14 academic centers worldwide [2]. It estimates the risk of sustained ventricular tachycardia in newly diagnosed patients who fulfill 2010 TFC for definite diagnosis of ARVC but have not experienced prior sustained ventricular arrhythmias. The aim of the individualized predictions is to aid patients and clinicians in their decision to implant an implantable cardioverter-defibrillator for primary prevention of sudden cardiac arrest.

Our prediction model is currently not part of any clinical guideline and should not be used to replace the standard of care. Please take into consideration that this model has not been validated in external cohorts. The estimated risk from our calculator is based on the population of patients included our original study and may not provide an accurate estimation in the specific circumstances of patients outside this cohort. The use and interpretation of the results provided by the calculator are at the responsibility of the user.

This calculator should not be used in patients with prior sustained ventricular arrhythmia or sudden cardiac arrest, as these were not included in the study cohort.

The predictions this calculator provides are based on clinical characteristics of patients at time of their diagnosis (within a time frame of ca. 1 year), therefore its application is meant for newly diagnosed patients (according to 2010 TFC). Pending further research, interpretation of predictions by entering characteristics during follow-up is discouraged.

Caution should be exercised when interpreting the prediction for patients <14 years of age, as the cohort this prediction model was based on only contained 2% pediatric patients <14 years.

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[1] Marcus FI, McKenna WJ, Sherrill D, Basso C, Bauce B, Bluemke DA, Calkins H, Corrado D, Cox MG, Daubert JP, Fontaine G, Gear K, Hauer R, Nava A, Picard MH, Protonotarios N, Saffitz JE, Sanborn DM, Steinberg JS, Tandri H, Thiene G, Towbin JA, Tsatsopoulou A, Wichter T, Zareba W. Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia: proposed modification of the Task Force Criteria. Eur Heart J 2010;31: .806–814. DOI: 10.1093/eurheartj/ehq025

[2] Cadrin-Tourigny J, Bosman LP, Nozza A, Wang W, Tadros R, Bhonsale A, etl al. A new prediction model for ventricular arrhythmias in arrhythmogenic right ventricular cardiomyopathy. European Heart J 2019. DOI: 10.1093/eurheartj/ehz103